Rare tumor-like masses in the vulva

DOI

https://dx.doi.org/10.18565/aig.2021.6.192-197

Zharov A.V., Kolesnikova E.V., Penzhoyan G.A., Dryaeva L.G.
1) Kuban State Medical University, Ministry of Health of the Russian Federation, Krasnodar, Russia; 2) Regional Clinical Hospital No 2, Ministry of Health of the Krasnodar Region, Krasnodar, Russia

Background. The reason for the increase in the rare pathology of the vulva is, firstly, the accumulation of genetic breakdowns in the population, the study of which has recently intensified, and, secondly, the possibilities of modern diagnosis, which allow for verifying the process, have improved. However, information about the rare tumor-like pathology of the vulva is still insufficient.
Objective. To optimize the diagnosis of rare tumor-like processes in the female external genitalia.
Case report. Based on international experience, the authors analyze their two own clinical cases. One patient had Behcet’s disease with a classic triad of symptoms; the other had aberrant breast tissue in the vulva. In both cases, the final diagnosis was made with a significant delay after the first signs of the disease appeared. The history data, that had not taken into account during the patients’ first visit and served as a reason for late diagnosis, were clarified. Complaints, the type of a pathological focus in the vulvar area, and clinical features are described.
Conclusion. The accumulation of genetic abnormalities in the population increasingly leads to their diverse phenotypic manifestations, inter alia with the localization in the vulva. For timely diagnosis and selection of the optimal treatment option, there is a need for the further accumulation of clinical experience and its coverage in the specialized medical literature.

Behcet’s disease

aberrant breasts

vulva

Full text (in Russian)

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Received 08.04.2021

Accepted 12.05.2021

Alexandr V. Zharov, PhD, MD (Medicine), Professor, Department of Obstetrics, Gynecology and Perinatology of the FPC and PPP, Kuban State Medical University, Ministry of Health of Russia, Krasnodar, Russian Federation. E-mail: zharov.1966@yandex.ru. ORCID: 0000-0002-5460-5959. 350063, Russia, Krasnodar, Sedina str., 4.
EkaterinaV. Kolesnikova, PhD (Medicine), Associate Professor, Department of Obstetrics, Gynecology and Perinatology of the FPC and PPP, Kuban State Medical University, Ministry of Health of Russia, Krasnodar, Russian Federation. E-mail: jokagyno@rambler.ru. ORCID: 0000-0002-6537-2572. 350063, Russia, Krasnodar, Sedina str., 4.
Grigory A. Penzhoyan, PhD, MD (Medicine), Professor, Head of the Department of Obstetrics, Gynecology and Perinatology of the FPC and PPP, Kuban State Medical University, Ministry of Health of Russia, Krasnodar, Russian Federation. E-mail: pga05@mail.ru. ORCID: 0000-0002-8600-0532. 350063, Russia, Krasnodar, Sedina str., 4.
Lyudmila G. Dryaeva, PhD (Medicine), Head of the Pathology Department of the Consultative and Diagnostic Center, Regional Clinic Hospital No 2, Krasnodar, Russian Federation. E-mail: Luda_dom@mail.ru. ORCID: 0000-0003-4927-6828. 350012, Russia, Krasnodar, Krasnykh Partizan str., 6/2.

For citation: Zharov A.V., Kolesnikova E.V., Penzhoyan G.A., Dryaeva L.G. Rare tumor-like masses in the vulva.
Akusherstvo i Ginekologiya/Obstetrics and Gynecology. 2021; 6: 192-197 (in Russian)
https://dx.doi.org/10.18565/aig.2021.6.192-197

Rare tumor-like masses in the vulva

Zharov A.V., Kolesnikova E.V., Penzhoyan G.A., Dryaeva L.G.

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