The features of the course of pregnancy and the outcomes of labor during cystinuria
Background. Cystinuria is an autosomal recessive hereditary disease associated with impaired transport of dibasic amino acids (including cystine) and with the formation of coral renal calculi, which is accompanied by frequent surgical interventions and recurrent pyelonephritis.Strizhakov A.N., Bogomazova I.M., Ignatko I.V., Belousova V.S., Timokhina E.V., Kardanova M.A., Kuznetsov A.S., Afanasyeva N.V., Samoilova Yu.A.
Case report. A primigravida patient was hospitalized for a period of 29-30 weeks with an exacerbation of chronic pyelonephritis of only one right working kidney. Combination treatment made it possible to prolong pregnancy up to 34 weeks. Early delivery is due to signs of renal failure.
Conclusion. Strict adherence to the rules of management of pregnant women with only one working kidney in the presence of chronic pyelonephritis could delay delivery to an optimal period in terms of minimizing perinatal complications.
Keywords
congenital cystinuria
urolithiasis
chronic pyelonephritis
only one working kidney
chronic renal failure
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Received 13.11.2018
Accepted 07.12.2018
About the Authors
Strizhakov, Alexander N., MD, academician of the Russian Academy of Sciences, professor, head of the Department of Obstetrics, Gynecology and Perinatologyof the Faculty of Medicine, I.M. Sechenov First Moscow State Medical University of the Ministry of Health of the Russian Federation (Sechenov University).
119991, Russia, Moscow, Trubetskaya str. 8-2. Tel.: +74997823045. E-mail: kafedra-agp@mail.ru
Bogomazova, Irina M., PhD, associate Professor of the Department of Obstetrics, Gynecology and Perinatology of the Faculty of Medicine, I.M. Sechenov First Moscow State Medical University of the Ministry of Health of the Russian Federation (Sechenov University).
119991, Russia, Moscow, Trubetskaya str. 8-2. Tel.: +74997823045. E-mail: kafedra-agp@mail.ru
Ignatko, Irina V., MD, corresponding member of the Russian Academy of Sciences, professor of the Russian Academy of Sciences, professor of the Department of Obstetrics, Gynecology and Perinatology of the Faculty of Medicine, I.M. Sechenov First Moscow State Medical University of the Ministry of Health of the Russian Federation
(Sechenov University). 119991, Russia, Moscow, Trubetskaya str. 8-2. Tel.: +74997823045. E-mail: iradocent@mail.ru
Belousova, Vera S., PhD, associate professor, associate professor of the Department of Obstetrics, Gynecology and Perinatology of the Faculty of Medicine, I.M. Sechenov First Moscow State Medical University of the Ministry of Health of the Russian Federation (Sechenov University).
119991, Russia, Moscow, Trubetskaya str. 8-2. Tel.: +74997823045. E-mail: kafedra-agp@mail.ru
Timokhina, Elena V., MD, associate professor, professor of the Department of Obstetrics, Gynecology and Perinatology of the Faculty of Medicine, I.M. Sechenov
First Moscow State Medical University of the Ministry of Health of the Russian Federation (Sechenov University).
119991, Russia, Moscow, Trubetskaya str. 8-2. Tel.: +74997823045. E-mail: kafedra-agp@mail.ru
Kardanova, Madina A., PhD, assistant professor of the Department of Obstetrics, Gynecology and Perinatology of the Faculty of Medicine, I.M. Sechenov First Moscow State Medical University of the Ministry of Health of the Russian Federation (Sechenov University).
119991, Russia, Moscow, Trubetskaya str. 8-2. Tel.: +74997823045. E-mail: kafedra-agp@mail.ru
Kuznetsov, Anton S., post-graduate student of the Department of Obstetrics, Gynecology and Perinatology of the Faculty of Medicine, I.M. Sechenov First Moscow State Medical University of the Ministry of Health of the Russian Federation (Sechenov University).
119991, Russia, Moscow, Trubetskaya str. 8-2. Tel.: +74997823045. E-mail: kafedra-agp@mail.ru
Afanasyeva, Natalia V., PhD, deputy chief physician for obstetrics and gynecology, S.S. Yudin City Clinical Hospital, Moscow Healthcare Department.
115446, Rassia, Moscow, Kolomensky proezd, 4. Tel.: +74997823064. E-mail: gkb-yudina@zdrav.mos.ru
Samoilova, Yulia A., PhD, head of the Department of Pregnancy Pathology of maternity hospital, S.S. Yudin City Clinical Hospital, Moscow Healthcare Department.
115446, Russia, Moscow, Kolomensky proezd, 4. Tel.: +74997823064. E-mail: gkb-yudina@zdrav.mos.ru
For citation: Strizhakov A.N., Bogomazova I.M., Ignatko I.V., Belousova V.S., Timokhina E.V., Kardanova M.A., Kuznetsov A.S., Afanasyeva N.V., Samoilova Yu.A. The features of the course of pregnancy and the outcomes of labor during cystinuria. Akusherstvo i Ginekologiya/Obstetrics and Gynecology. 2019; (4): 108-112. (in Russian)
https://dx.doi.org/10.18565/aig.2019.4.108-112
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