Pregnancy and successful vaginal birth in a patient with Swyer syndrome
Pasman N.M., Pismak M.A., Bukhtueva N.G., Shaklein A.V.
Background: Swyer syndrome is a pure gonadal dysgenesis and is an extremely rare condition. Given that a patient with this syndrome can only become pregnant after in vitro fertilization, and delivery is usually performed by caesarean section, the publication of the experience of managing a patient with Swyer syndrome and vaginal delivery is of interest to practical obstetrics and gynecology.
Case report: A 33-year-old female patient diagnosed with Swyer syndrome in 2007 became pregnant after in vitro fertilization. The patient had a poor obstetric and past history. There was a threat of early termination of pregnancy, the patient was diagnosed with gestational diabetes at 12 weeks gestation. At 39 weeks gestation, the patient went into spontaneous labor. The patient gave birth to a live full-term girl weighing 3780 g, 53 cm in length, with an Apgar score of 8/9. The postpartum period was uneventful.
Conclusion: The obstetric situation should guide the choice of mode of delivery for patients with Swyer syndrome. The presence of this syndrome does not rule out the possibility of vaginal birth in the event of spontaneous labor.
Authors' contributions: Pasman N.M. – developing the concept and design of the study, scientific editing of the text;
Pismak M.A. – developing the design of the study, working with literature sources, writing the text; Bukhtueva N.G. – developing the design of the study, editing the text; Shaklein A.V. – delivery of the patient.
Conflicts of interest: The authors declare no possible conflicts of interest.
Funding: The study was conducted without sponsorship.
Patient Consent for Publication: The patient provided an informed consent for the publication of her data.
For citation: Pasman N.M., Pismak M.A., Bukhtueva N.G., Shaklein A.V.
Pregnancy and successful vaginal birth in a patient with Swyer syndrome.
Akusherstvo i Ginekologiya/Obstetrics and Gynecology. 2025; (1): 150-153 (in Russian)
https://dx.doi.org/10.18565/aig.2024.233
Keywords
References
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Received 16.09.2024
Accepted 27.12.2024
About the Authors
Natalia M. Pasman, Dr. Med. Sci., Professor, Head of the Department of Obstetrics and Gynecology of the Institute of Medicine and Medical Technologies, Faculty of Medicine and Psychology, Novosibirsk State University, 630090, Russia, Novosibirsk, Pirogova str., 2, +7(913)916-25-91, nmpasman@gmail.com,https://orcid.org/0000-0002-6095-1954
Maria A. Pismak, student at the Department of Obstetrics and Gynecology of the Institute of Medicine and Medical Technologies, Faculty of Medicine and Psychology, Novosibirsk State University, 630090, Russia, Novosibirsk, Pirogova str., 2, +7(961)716-97-19, m.pismak@g.nsu.ru
Natalia G. Bukhtueva, Senior Lecturer at the Department of Obstetrics and Gynecology of the Institute of Medicine and Medical Technologies, Faculty of Medicine and Psychology, Novosibirsk State University, 630090, Russia, Novosibirsk, Pirogova str., 2; obstetrician-gynecologist at the Obstetric Observational Department No. 1,
City Clinical Hospital No. 1, 630047, Russia, Novosibirsk, Zalesskogo str., 6, +7(913)776-06-86, _nataliya_77@mail.ru
Aleksandr V. Shaklein, Dr. Med. Sci., Associate Professor at the Department of Obstetrics and Gynecology of the Institute of Medicine and Medical Technologies, Faculty of Medicine and Psychology, Novosibirsk State University, 630090, Russia, Novosibirsk, Pirogova str., 2; Deputy Chief Physician, City Clinical Hospital No. 1, 630047, Russia, Novosibirsk, Zalesskogo str., 6, +7(913)921-54-02, a.shaklein@g.nsu.ru
Corresponding author: Maria A. Pismak, m.pismak@g.nsu.ru